Rapunzel Syndrome: Rare 'Tale' of a Broken 'Tail'.
نویسندگان
چکیده
BACKGROUND Rapunzel syndrome is a rare and unique form of trichobezoar, in which a cast of hairs is formed in the stomach with its 'tail' extending up to varying lengths into the small bowel. Almost all cases described in literature are of 'classic' and more common form of Rapunzel. Sometimes however, the tail of bezoar is broken into smaller fragments. There is not much literature available on this rarer subset of Rapunzel syndrome. CASE REPORT In this report we present the ultrasound (USG) and CT findings of a case of Rapunzel syndrome in which the tail had broken into five separate fragments. The patient presented clinically with intestinal obstruction due to the impaction of the distal- most fragment in the ileum. CONCLUSIONS Our case highlights the fact that although USG features may be suggestive, a careful evaluation of CT images is essential for a confidant preoperative diagnosis of Rapunzel syndrome. In cases of this syndrome with a broken tail, CT is essential for precise count and localization of the separated fragments to ensure their complete removal at the time of surgery. We also propose to name the fragments of the broken tail as 'bezoarlets'. This word aptly describes the tail fragments as it suggests their origin from the larger gastric bezoar and the suffix 'lets' conveys they are smaller in size.
منابع مشابه
Rapunzel Syndrome of a Cotton Bezoar in a Multimorbid Patient
Bezoars are foreign bodies that form masses in the gastric or intestinal lumen, particularly in mentally retarded or psychiatric patients. Classifications of bezoars are made according to the content of the bezoar, such as trichobezoars (of hairs), phytobezoars (of vegetable fibers), lactobezoars (of milk products), and others containing medications or other foreign materials. Whatever the etio...
متن کاملAn unusual presentation of Rapunzel syndrome, a double impacted trichobezoar
Bezoars are collections of interwoven organic or inorganic matter found in the alimentary canal. Rapunzel syndrome represents a rare presentation of trichobezoar where the tail of main gastric bezoar extends into the lumen of small intestine. We present the case of a 09 year old female child who presented to us as a case of acute intestinal obstruction as a rare manifestation of Rapunzel syndro...
متن کاملA Case of Rapunzel Syndrome
Rapunzel syndrome refers to a very rare condition in which swallowed hair forms a gastric trichobezoar that has a long tail extending into the small bowel. We describe a case of Rapunzel syndrome in an 8-year-old girl who presented with abdominal mass, epigastric pain and vomiting. Abdominal computed tomography scan showed a markedly dilated stomach filled with coarse heterogeneous materials. U...
متن کاملA Case Report
Rapunzel syndrome is very rare gastric foreign bodies that occur in children. It is a severe condition of a gastric trichobezoar with a long tail that passes into the small intestine. Here, we present the case of an 8-year-old girl with Rapunzel syndrome due to a very large (7 × 7 × 30 cm) gastric trichobezoar. The patient had trichotillomania and trichophagia for 1 year prior to presentation. ...
متن کاملRapunzel syndrome reviewed and redefined.
Rapunzel syndrome is a rare presentation of a trichobezoar, with 24 cases having been reported in literature so far. This syndrome has been reported in 23 female and 1 male patient with a mean age of 10.8 years. The patients commonly present with abdominal pain, nausea, vomiting and signs of obstruction. The distal end of the bezoar may be in the jejunum, ileum or the colon. We evaluate the var...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید
ثبت ناماگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید
ورودعنوان ژورنال:
- Polish journal of radiology
دوره 81 شماره
صفحات -
تاریخ انتشار 2016